Klinefelter′s syndrome associated with progressive muscular atrophy simulating Kennedy′s disease

Progressive Muscular Atrophy

a crack-like ulceration at the junction of the skin and mucous membrane in the two sides of the nose alternately?recurrent attacks of these two complainta during JDecember-January last in a case of progressive muscular atrophy was treated and cured with Bi, plunocaine and sulfanilamide mixed with honey. Was it correct to think that these troubles were of a trophic origin ? As to the P.M.A. the ...

Progressive Muscular Atrophy

Electromyographic analysis in spinal progressive muscular atrophy, juvenile unilateral muscular atrophy, neural progressive muscular atrophy and myeloradiculoneuritis.

Recently, as diagnostic aids of neurological science, not only electromyography but also other techniques such as motor nerve conduction velocity, evoked potentials and strength-duration curve have been performed. In this paper, the first, the standard value of conduction velocities and the critical value of reduced conduction velocities in pathologic condition were discussed, because the probl...

Disease course and prognostic factors of progressive muscular atrophy.

OBJECTIVE To investigate the natural history and prognostic factors in patients with nonhereditary, adult-onset progressive muscular atrophy. DESIGN Inception cohort conducted for 18 months. Settings Three university hospitals in the Netherlands (referral centers for neuromuscular diseases). Patients Thirty-seven consecutive patients newly diagnosed (onset of weakness <4 years) with progressi...

Anti-Ma2 associated paraneoplastic neurological syndrome presenting as encephalitis and progressive muscular atrophy.

A 36 year old man with a history of testicular germ cell tumour presented six months after bilateral orchidectomy with progressive amnesia, irritability, vertical gaze palsy, and generalised seizures. Eight months after initial onset of symptoms, he demonstrated a head drop with muscular atrophy of the upper limbs, shoulder girdle, and posterior neck. He reported no sensory disturbances and his...